Ulcerative jejunitis, an unusual symptom of IgA vasculitis, in a pediatric patient
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Abstract
Immunoglobulin A vasculitis (IgA vasculitis) is the most common vasculitis, occurring in children and peaking between 4 and 6 years of age. Diagnosis is based on clinical manifestations in 95% of cases, based on the EULAR/PRINTO/PRES criteria, such as skin rashes along with other gastrointestinal, musculoskeletal, and renal disorders. Occasionally, an atypical presentation may occur, necessitating diagnosis by biopsy of the affected organ indicating IgA deposition. Treatment is conservative, as it is self-limiting in most cases and resolves within weeks. Mortality is related to long-term renal impairment.
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References
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