Use of pentoxifylline in lipoidoproteinosis or Urbach's disease A case report
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Abstract
Introduction: Lipoproteinosis, or Urbach's disease, Wiethe, is a genodermatosis of genetic origin with an autosomal recessive transmission pattern without sex predilection. It is characterized by varying degrees of intercellular deposits of hyaline material in the skin, mucous membranes, and internal organs, leading to infiltration and thickening of affected organs. The course is slow and benign.
Clinical case: The case of a 6-year-old girl who consulted for dry skin and hoarseness since she was two years old is presented. The clinical and histopathological diagnosis is made.
Evolution: Treatment with pentoxifylline was started, and a significant improvement in the lesions was observed after six months.
Conclusions: The efficacy and safety of pentoxifylline as a complementary therapy in pediatric patients diagnosed with lipoidoproteinosis are demonstrated.
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References
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